详情 |
英文名称 |
Anti-ACADS Polyclonal Antibody |
中文名称 |
酰基辅酶A脱氢酶短链抗体 |
靶标 |
ACADS |
别名 |
ACAD3, Acyl Coenzyme A dehydrogenase, C2 to C3 short chain, Acyl-CoA dehydrogenase, C2 to C3 short chain, Acyl-CoA dehydrogenase, short chain, Acyl-Coenzyme A dehydrogenase, short chain, AI196007, Bcd-1, Bcd1, Butyryl CoA dehydrogenase, EC 1.3.99.2, SCAD, Short chain acyl CoA dehydrogenase, Short-chain specific acyl-CoA dehydrogenase, mitochondrial, Unsaturated acyl CoA reductase, ACADS_HUMAN |
背景资料 |
This gene encodes a a tetrameric mitochondrial flavoprotein, which is a member of the acyl-CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl-CoA Dehydrogenase Deficiency. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults. |
Swiss Prot |
P16219 |
Gene ID |
35 |
亚细胞定位 |
Cytoplasm |
宿主 |
Rabbit |
克隆类型 |
Polyclonal Antibody |
亚型 |
IgG |
蛋白分子量 |
44kDa |
稀释比例 |
WB 1:200-1000. IHC 1:25-100. |
免疫原 |
Recombinant protein of human ACADS |
纯化方法 |
Affinity purification |
储存液 |
Buffer: pH7.4 PBS, 0.05% NaN3, 40% Glycerol |
保存 |
Store at -20°C. Avoid freeze / thaw cycles. |
交叉反应 |
Human Rat Mouse |
应用 |
WB IHC |
规格 |
50ul 100ul |
单位 |
支 |
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